Answer:
Based on the given information , the cellular structure , which don not function properly in Tay Sachs disease is <u>Lysosomes </u>
Explanation:
<u>LYSOSOMES -:</u> In many animal cells, a lysosome is a membrane-bound organelle. These are spherical vesicles containing hydrolytic enzymes that can break down many types of biomolecules. A lysosome, with both its membrane proteins and its lumenal proteins, has a particular composition. There are a number of enzymes in lysosomes, helping the cell to break down different biomolecules that it swallows, including peptides, nucleic acids, carbohydrates , and lipids (lysosomal lipase). For optimal function, the enzymes responsible for this hydrolysis need an acidic environment.
<u>TAY SACHS DISEASE -: </u>The autosomal recessive disorder Tay-Sachs is caused by mutations in both gene alleles (HEXA) on chromosome 15. HEXA codes for the enzyme β-hexosaminidase A alpha subunit. This enzyme is contained in organelles, lysosomes, which break down large molecules for the cell to recycle.
Normally, β-hexosaminidase A helps to degrade a lipid called ganglioside GM2, but the enzyme is absent or present only in very small amounts in Tay-Sachs individuals, enabling excessive accumulation of ganglioside GM2 in neurons. In the different types of Tay-Sachs, the progressive neurodegeneration seen depends on the speed and degree of accumulation of GM2 ganglioside, which in turn depends on the amount of functional β-hexosaminidase A present in the body.
Hence , the answer is<u> lysosomes .</u>
The answer would be B as penicillin is derived from Penicillium fungi.
<span>AAU-Aspargine GGC-Glycine UAC- Tyrosine
</span>
Answer:
1.) Compounds that contain a fused ring systerm are called _steroids_. These have three 6-membered rings and one 5-membered ring. some of these compounds are found in biological membranes.
2.) _Fatty acids__ are the building blocks for many lipids, and they generally contain an even number of carbon atoms and an unbranched hydrocarbon chain
3.) _Glycolipid__ are formed when a carbohydrate is glycosidically linked to a hydroxyl group of a lipid. examples include gangliosides and cerebrosides. these are also found in biological membranes.
4.) _Triacylglycerols_are the storage form of lipids, accumulating in adipose tissue, and they can be used as metabloic fuel. these compounds have a polar part, made of three ester groups, and a nonpolar fatty acid tail.
5.) _Sphingolipids__ are made up of a long-chain amino alcohol joined, either by a glycosidic linkage or a phosphodiester linkage, to a fatty acid. these do not contain _glycerol__. they are abundant in the nervous system.
6.) When glycerol esterified to two fatty acids and a phophoric acid molecule a _glycerophospholipid_ is formed. These are found in biological membranes.
